627 Matching Annotations
  1. Jan 2020
    1. atrial septal defect
    2. large ears
    3. Open mouth appearance
    4. Short philtrum
    5. Long face
    6. Hypotonia
    7. intellectual disability
    8. Developmental delay
    1. down-slanting eyelid
    2. short proximal extremities
    3. 3
    4. 3
    5. 8
    6. 5
    7. 8
    8. 5
    9. 4
    10. 6
    11. 8
    12. 5
    13. 3
    14. 6
    15. 5
    16. 3
    17. 3
    18. 3
    19. 2
    20. 6
    21. 8
    22. 6
    23. 5
    24. 3
    25. 6
    26. 2
    27. macrocephaly
    28. macrocephaly
    29. macrocephaly
    30. 7
    31. 2
    32. 5
    33. 1
    34. 5
    35. 1
    36. 5
    37. 1
    38. 1
    39. 1
    40. 1
    41. muscular hypotonia
    42. muscular hypotonia
    43. muscular hypotonia
    44. muscular hypotonia
    45. muscular hypotonia
    46. muscular hypotonia
    47. seizures
    48. intellectual disability
    49. intellectual disability
    50. intellectual disability
    51. intellectual disability
    52. motor development
    53. motor development
    54. motor development
    55. motor development
    56. motor development
    57. motor development
    58. speech and language development
    59. speech and language development
    60. speech and language development
    61. speech and language development
    62. speech and language development
    63. developmental delay
    64. developmental delay
    65. developmental delay
    66. developmental delay
    67. developmental delay
    68. developmental delay
    1. primary infertility
  2. Dec 2019
    1. acute respiratory failure
    2. 54.0 cm (99th percentile)
    3. 2 cm (in acute setting)
    4. hyperechoic cortex of both kidneys
    5. aortic insufficiency
    6. +
    7. +
    8. Platyspondyly
    9. +
    10. +
    11. +
    12. <3rd percentile
    13. Splenomegaly
    14. <3rd percentile
    15. elevated methionine
    16. talipes equinovarus
    17. Neonatal jaundice
    1. failure to thrive
    2. hyperkinetic
    3. nystagmus
    4. right esotropia
    5. cortical edema
    6. downward gaze deviation
    7. tongue thrusting
    8. axial hypotonia
    9. appendicular spasticity
    10. could not verbalize
    11. lost voluntary mobility
    12. bilateral nonsynchronous spikes
    13. short non-provoked generalized tonic-clonic seizures
    14. intractable epilepsy
    15. ataxia
  3. Nov 2019
    1. hypertrophy of slow fibres
    2. fibre degeneration
    3. interstitial fibrosis
    4. hypertrophy of Type 1 (slow) fibres
    5. nemaline rods
    6. selective and marked atrophy of Type 2 (fast) fibres
    7. nasogastric tube feedin
    8. bulbar weakness
    9. non-invasive ventilation
    10. respiratory muscle weakness
    11. thoracic scoliosis
    12. thoracic scoliosis
    13. bilateral hip dislocation
    14. finger contractures
    15. knee contractures
    16. high arched palate
    17. hypotonia
    18. limb muscles
    19. weakness of facial
    20. rocker-bottom
    21. bilateral talipes
    22. overlapping digits
    23. overlapping digits
    24. polyhydramnios
  4. Oct 2019
  5. Sep 2019
    1. if n is very small (for example n = 3), rather than showing error bars and statistics, it is better to simply plot the individual data points.
    1. allele id lookup result

    2. Seizures
    3. 22 mo
    4. variant id lookup result

    5. constipation
    6. hairy elbows
    7. strabismus
    8. joint laxity
    9. fetal fingerpads
    10. mild hypertelorism
    11. long eyelashes
    12. mild exophthalmos
    13. broad forehead
    14. triangular face
    15. aggressivity
    16. no eye contact,
    17. social interaction
    18. autistic
    19. yes
    20. severe
    21. no speech
    1. I 1

      CaseI1-2: Case I1 is the asymptomatic paternal grandfather of proband 2 in family 2. The heterozygous Thr295Ile substitution was found in this individual.

      CasePresentingHPOs: HP:0005543, (Reduced protein C activity)

      HPOsFreeText: Protein C activity was reduced: Normal range = 70-140% (actual = 39%). Patient also had reduced protein C antigen: Normal range = 70-130% (Actual=36%).

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This individual was asymptomatic.

      CasePMIDs:

    2. grandmother (I3) of Proband 2

      CaseI3-2: Case I3 is the asymptomatic grandmother of proband 2 in family 2. The heterozygous Leu-34Pro substitution was found in this individual.

      CasePresentingHPOs: HP:0005543, (Reduced protein C activity)

      HPOsFreeText: Protein C activity was reduced: Normal range = 70-140% (actual = 48%). Patient also had reduced protein C antigen: Normal range = 70-130% (Actual=36%).

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This individual was asymptomatic.

      CasePMIDs:

    3. asymptomaticmother (II4

      CaseII4-2: Case II4 is the asymptomatic mother of proband 2 in family 2. The heterozygous Leu-34Pro substitution was found in this individual.

      CasePresentingHPOs: HP:0005543, (Reduced protein C activity)

      HPOsFreeText: Protein C activity was reduced: Normal range = 70-140% (actual = 55%). Patient also had reduced protein C antigen: Normal range = 70-130% (Actual=34%).

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This individual was asymptomatic.

      CasePMIDs:

    4. paternal relatives II2

      CaseII2-2: Case II2 is the asymptomatic paternal uncle of proband 2 in family 2. The Thr295Ile substitution was found in this individual.

      CasePresentingHPOs: HP:0005543, (Reduced protein C activity)

      HPOsFreeText: Protein C activity was reduced: Normal range = 70-140% (actual = 44%). Patient also had reduced protein C antigen: Normal range = 70-130% (Actual=33%).

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This individual was completely asymptomatic.

      CasePMIDs:

    5. he asymptomatic fatherof Proband 2 (II3)

      CaseII3-2: Case II3 is the clinically asymptomatic father of proband 2 in family 2. The Thr295Ile substitution was found in this individual.

      CasePresentingHPOs: HP:0005543, (Reduced protein C activity)

      HPOsFreeText: Protein C activity was reduced: Normal range = 70-140% (actual = 43%). Patient also had reduced protein C antigen: Normal range = 70-130% (Actual=34%).

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This individual was completely asymptomatic.

      CasePMIDs:

    6. Proband 2

      CaseIII1-2: Proband 2 (Case III 1 family 2) was a 19 year old male diagnosed with deep vein thrombosis in both legs since the age of 16. The family of this individual was asymptomatic with respect to thrombolytic disease and was non-consanguineous.

      CasePresentingHPOs: HP:0002625, HP:0005543, HP:0004936, (Deep venous thrombosis), (Protein C deficiency), (Venous thrombosis),

      HPOsFreeText: Deep vein thrombosis was in both legs since age of 16. This patient also had low protein C antigen.

      CaseNotHPOs:

      NotHPOsFreeText:

      CaseAddInfo: This Case (Case III1-2) was designated as Proband 2.

      CasePMIDs:

    7. the father (I1) of Proband 1

      CaseI1-1: Case I1-1 is a 54 year-old male from Family 1. This individual has a heterozygous Asp255His mutation and is the father of the proband (II1-1). This individual was asymptomatic and lab results were within normal ranges.

      CasePresentingHPOs:

      HPOsFreeText:

      CaseNotHPOs:

      NotHPOsFreeText: Patient was completely asymptomatic.

      CaseAddInfo:

      CasePMIDs: